produced inGERMANY

For the Dietary Management of disorders inbranched chain amino acid metabolism inCHILDREN OVER 1 YEAR OF AGE, ADOLESCENTS AND ADULTS

• Leucine, isoleucine and valine free amino acid mixture• Contains high proportion of protein supplement in low volume, free from sucrose• Supplemented with vitamins, minerals and trace elements• Easy to prepare

DESCRIPTIONcomida-MSUD B is an isoleucine, leucine and valine free protein supplement for the dietary management of disorders in branched chain amino acid metabolism in children over 1 year of age, adolescents and adults.comida-MSUD B is supplemented with vitamins, minerals and trace elements.

INDICATIONSFor the dietary treatment in children over 1 year of age, adolescents and adults with disorders in metabolism of branched chain amino acids, such as Maple Syrup Urine Disease (MSUD).

RECOMMENDED USEThe daily amount of comida-MSUD B needed depends on age, body weight and individual metabolic condition.The dose of comida-MSUD B is to be monitored and adjusted by the physician regularly.The daily amount required should be divided into 3 to 5 single portions and should be taken mixed also with food or beverages allowed in calculated amounts.

IMPORTANT NOTICE:• Not suitable as sole source of nutrition • Must be used under medical supervision• Not to be used by individuals without disorders in branched chain amino acid metabolism • For children over 1 year of age, adolescents and adults with disorders in branched chain amino acid metabolism • Not suitable for parenteral use comida-MSUD B is free from any preserving agent, colourings or sweeteners

Food for SpecialMedical Purposes

Ingredients: Maltodextrin, L-Lysine-L-Glutamate, L-Proline, L-Glutamine, L-Arginine-L-Aspartate, Potassium-L-Glutamate, L-Serine, L-Lysine- L-Aspartate, L-Threonine, L-Alanine, L-Phenylalanine, tri-Calcium phosphate, L-Tyrosine, Magnesium-L-Aspartate, L-Cystine, L-Histidine, di- Calcium phosphate, Choline bitartrate, L-Tryptophan, Glycine, L-Methionine, Sodium chloride, Magnesium carbonate, Vitamins (A, D, E, K, C, B1, B2, Niacin, B6, Folic acid, Pantothenic acid, B12, Biotin), Inositol, L-Carnitine-L-Tartrate, Taurine, Vanillin, Iron-II-sulfate, Zinc sulfate, Manganese sulfate, Copper sulfate, Sodium fluoride, Sodium molybdate, Potassium iodide, Chromium-III-chloride, Sodium selenite.

Minerals per 100 gSodium mg 556Potassium mg 1255Chloride mg 858Calcium mg 2063Phosphorus mg 1217Magnesium mg 302Iron mg 28Trace elementsZinc mg 19Copper µg 2174Iodine µg 311Chromium µg 62Fluoride µg 373Manganese µg 4348Molybdenum µg 168Selenium µg 75VitaminsVitamin A (RE) µg 1247Vitamin D µg 19Vitamin E (α-Tocopherol) mg 22Vitamin K µg 68Vitamin C mg 168Vitamin B1 µg 2050Vitamin B2 µg 2796Niacin mg 28Vitamin B6 µg 1864Folate (DFE) µg 518Pantothenic acid mg 17Vitamin B12 µg 3,7Biotin µg 62L-Carnitine mg 155Choline mg 807Inositol mg 280Taurine mg 155

Nutrition facts per 100 gEnergy kJ / kcal 1238 / 291

Fat (of which) g < 0,5

saturated fatty acids g < 0,1

Carbohydrates g 11

of which Sugar g 0,8

of which Maltodextrin g 9,9

Protein equivalent * g 62

Salt g 1,4

Amino acids g 75

L-Alanine g 4,1

L-Arginine g 3,7

L-Aspartic acid g 7,1

L-Cystine g 2,3

L-Glutamic acid g 9,1

L-Glutamine g 8,1

Glycine g 1,7

L-Histidine g 2,3

L-Lysine g 6,9

L-Methionine g 1,7

L-Phenylalanine g 4,0

L-Proline g 8,5

L-Serine g 5,1

L-Threonine g 4,6

L-Tryptophan g 1,8

L-Tyrosine g 3,7* Conversion: 1 g Protein= 1,2 g Amino acids = 17 kJ = 4 kcal