rheumatology · 2021. 1. 14. · rheumatology pocket guide v1020 friends of the foundation a...
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SUPPORT FOR YOU FROM THE
PULMONARY FIBROSIS FOUNDATION
The Pulmonary Fibrosis Foundation mobilizes people and resources to provide access to high quality care and leads research for a cure so people with pulmonary fibrosis will live longer, healthier lives.
To learn more about how the PFF can help support you, contact the PFF Patient Communication Center at 844.TalkPFF (844.825.5733) or [email protected], or visit the PFF online at pulmonaryfibrosis.org.
SPONSORED BY:
© 2020 PULMONARY FIBROSIS FOUNDATION. ALL RIGHTS RESERVED.
RH
EU
MA
TO
LO
GY
PO
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GU
IDE
v1020
FRIENDSOF THE FOUNDATION
A multidisciplinary discussion (MDD) for patients suspected to have CTD-ILD has many benefits and is crucial to the diagnostic process. MDD can increase diagnostic confidence by refining a provisional diagnosis, enhance interobserver agreement on the diagnosis, and increase diagnostic precision. It is important that CTD patients with evidence of respiratory disease are referred to a pulmonologist. In addition to rheumatology and pulmonary, other areas of specialty that are often involved in MDD for CTD-ILD include thoracic radiology, and pathology. Patients benefit from improved care coordination when MDD is utilized.
Understanding Connective Tissue Disease-Related Interstitial Lung Disease
Rheumatology
Thoracic Radiology Pathology
Pulmonary
Respiratory Therapy
*HRCT images courtesy of Gregory P. Cosgrove, MD
Mitto S, Fell CD. Semin Respir Crit Care Med 2014;35:249.
Organizing pneumonia (dense ground glass)
Reticulation (lines)
Ground glass
Traction bronchiectasis
Acknowledgements Elizabeth Volkmann, MD, MS University of California, Los Angeles Medical Center Los Angeles, CA
TA
BL
E 1
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IAG
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AT
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EV
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k fa
cto
rs o
n h
isto
ry
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d p
hy
sic
al
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e se
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e N
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tern
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ore
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ly
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ted
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hic
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istin
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e ch
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en in
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ymm
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c,
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ron
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bro
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ub
ple
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l sp
arin
g.1
1 Ref
eren
ces:
Cap
ob
ian
co J
, et a
l. R
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gra
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ics
201
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uja
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t al.
Rad
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elle
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Ris
k fa
cto
rs b
ase
d o
n
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ora
tory
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die
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an
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ntib
od
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ntib
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(PL1
) an
tibo
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ntib
od
y P
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tibo
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tibo
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tibo
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ti-S
mith
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tibo
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*
Sy
mp
tom
s
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ly-
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ue/
Dys
pn
ea
on
exe
rtio
n
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e-
Dys
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ea a
t res
t
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y p
atie
nts
are
as
ymp
tom
atic
in
early
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Sym
pto
ms
may
b
e n
on
spec
ific
Cer
tain
CT
Ds
hav
e sp
ecifi
c ris
k fa
cto
rs fo
r IL
D a
s d
escr
ibed
in
Tab
le 2
.
Clu
es
Tip
s
Sig
ns
Cra
ckle
s o
n
ausc
ulta
tion
Dig
ital c
lub
bin
g
Oxy
gen
des
atu
ratio
n
with
exe
rcis
e o
r at r
est
Ear
ly in
co
urs
e o
f IL
D,
PF
Ts m
ay b
e n
orm
al,
or t
her
e m
ay b
e an
is
ola
ted
dec
reas
e in
th
e D
LCO
NS
IP is
the
m
ost
co
mm
on
ra
dio
gra
ph
ic p
atte
rn
of I
LD
in C
TD
Ra
dio
gra
ph
ic
Hig
h-r
eso
lutio
n c
hes
t CT
fin
din
gs
con
sist
ent w
ith IL
D
Ret
icu
latio
n (p
erip
her
al “l
ines
” in
the
sub
ple
ura
l sp
ace)
Gro
un
d g
lass
(haz
y) o
pac
ities
an
d/o
r Tra
ctio
n b
ron
chie
ctas
is
(dila
tion
of t
he
airw
ays
larg
er th
an
the
adja
cen
t blo
od
ves
sel)
Ho
ney
com
b c
han
ge
(per
iph
eral
, su
bp
leu
ral “
cyst
s” in
row
s)
Ph
ysi
olo
gic
Res
tric
tive
pat
tern
o
n P
FTs
- L
ow
FV
C
- Lo
w T
LC
Diff
usi
on
Imp
airm
ent
- Lo
w D
LCO