mayer rokitansky kuster hauser syndrome
TRANSCRIPT
I was brought into this world from the womb of my mother…………………………
I am a female baby………..
I thought…… I am a
girl…… but the thought
remained as a thought in my life…………………
The period when she realized that she is different from all other girls…………
She did not have something which others had………….
The day when she knew that she had…………
MAYER ROKITANSKY KUSTER HAUSER
SYNDROME
Imagine what it is for a woman to know that she has no uterus and no vagina….
it’s TERRIBLE………..
Named after……..
August Franz Joseph Karl Mayer Carl Frieherr von Rokitansky Hermann Kuster G.A .Hauser
A rare disorder characterized by congenital absence of uterus and vagina
You cry because of pain but they cry because…………………….
THEY DON’T
HAVE PAIN………
Will u stop menstruating if you could?????
…………………a question asked by a
MRKH girl to all normal women who complain about menstruating……………….
Prevalence
1 in 4000-5000 female births
IS IT MY FAULT?
The cause is unknown……… a blank space still
remains…..
Can you find the answer?........
Signs & Symptoms……
Primary amenorrhea Complete or partial absence of cervix, uterus
and vagina Painful coitus Hormonally normal Enters puberty with development of
secondary sexual characteristics-adrenarche , thelarche
Chromosomal constellation-46XX Ovaries intact…………ovulation
occurs………………….
But she cannot be……… A MOTHER she cannot carry………. A life in her
womb A life perhaps incomplete………
Forms of MRKH…..
Only absence of vagina and uterus Absence of uterus and vagina + 40% kidney
abnormalities 10% hearing
problems 10-12%
skeletal abnormalities
Solution?
No treatment to let the woman herself become pregnant
Treatment available to make the intercourse comfortable
Surgical Management
Frank technique or perineal dilation apply progressive pressure
to the perineum using a bicycle-seat stool to hold a dilator in place .
…………compliance may be poor………..
McIndoe technique
Split thickness skin graft -skin from thigh or buttocks is used……..
PROCEDUREPocket created between rectum and urethra ↓Place a cylindrical stent covered with skin
graft ↓Fix graft in place by attaching cut edges of
skin incission
↓Labia majora sutured loosely together ↓ 1 week later remove stent ↓ irrigate vagina and cauterize areas of
granulation with silver nitrate sticks
Keep dilator in neovagina every day and night for 3 months;
followed by every night for next three
months………….scarring at donor site………………….neovaginal stenosis…………………….long term dilation……………
Williams Vaginoplasty
Uses vulval flap to make a vaginal tube………needs long term dilation……..
Rotational Flap Procedure
Uses - pudendal thigh - gracilis myocutaneous - labia minora - other fasciocutaneous flaps………..extensive scarring at donor
site……..………...requires patient’s
diligence…………...
Intestinal Neovagina
Uses isolated segment of bowel for vagina; mostly sigmoid
………..high grade of satisfaction……….
Vecchietti Technique
Exert continuous progressive pressure…….. by acrylic olive passed through potential neovaginal space and abdominal wall……..
↓Traction device placed into peritoneal cavity ↓ Draw olive upward ………done laparoscopically………..
Options…….
My baby in other’s womb………SURROGACY
Means……
Surrogacy is an arrangement in which a woman carries and delivers a child for another person or couple……..
Surrogacy varies…….
Traditional surrogacy: woman may be child’s genetic mother
Gestational surrogacy: carry pregnancy to delivery after having an embryo, with no genetic relationship, transferred to her uterus
Commercial surrogacy Altruistic surrogacy
Think of IVF if both have problem…………
Characteristics of a surrogate mother
Relative or close friendBetween 21 and 38 yrs of ageGiven birth to one or more child
previously with no complicationsNo history of STDsGood health………
Average weight for her height A non-smoker who lives in a smoke
free room No illegal drug use
Arguements
Cost of surrogacy Custody Desperate needs home Long process Feel of Guilt
Promise of a mother……
First Major Groundbreaking Surrogacy
Publicized issue of Melissa Stem in 1986, USA…… Biological father: William Stem His wife : Elizabeth Stem Surrogate Mother: Mary Beth
Whitehead
Mary Beth Whitehead is the biological mother………..legal mother…………
Who is the Mother?????
Saudi Arabia sanctioned world’s first Uterus transplant……..
In India……
Commercial surrogacy legal in India……Supreme Court in 2002
leader in international surrogacy……
Contact…….
www.surrogatemothers.comwww.surrogateAlternatives.comwww.GlobalDoctorOptions.comwww.indiansurrogates.com
I didn’t bring you……. butI will build you……..
You are my baby and am your mother….
Adoption……
Life is Life……
Realize what you have………… There are people on earth
around you carrying pain in heart ……….
may be more than yours…….
A relation sopure……
Thank you………..