mahmoud aly rageh , md.€¦ · congenital esotropia * essential infantile esotropia *idiopathic...

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1/29/2018 1 *Mahmoud Aly Rageh , MD. *Research Institute of Ophthalmology. * *Esotropia Occuring during the first 6 months of life.

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Page 1: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

1

*Mahmoud Aly Rageh , MD.

*Research Institute of Ophthalmology.

*

*Esotropia Occuring during the

first 6 months of life.

Page 2: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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**Congenital Esotropia

*Essential infantile Esotropia

*Idiopathic infantile Esotropia

*Early onset Esotropia

*Early Acquired Esotropia

*Ciancia’s syndrome

*

*Subject of much debate with regard

to its naming, diagnostic features ,

treatment and its onset.

Page 3: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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*

*

*

Page 4: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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*

*Large size 15 degrees or more.

*Stable

*Variable.

*No CNS anomalies

*Pseudo defective abduction

*Inferior oblique overaction

*DVD

*Latent and manifest latent nystagmus

Page 5: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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*

*

Page 6: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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*

*Affecting either eye or cross fixation

*

*Any state of refraction

Page 7: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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*

*Unknown

*

*Accommodative in 15%

*Hypertonic medial recti without nystagmus.

*Hypertonic medial recti with nystagmus.

*(Nystagmus blockage syndrome-Ciancia’s

Syndrome)

Page 8: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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*

*Botulinum toxin

*Bimedial recession

*

*Recently between 6 and 9 months

(American School)

Page 9: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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*

*Microtropia of 10 prism diopters with

peripheral fusion and gross stereopsis

*

*

Page 10: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

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*

*Between one and two years

*

*

Page 11: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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*

*Penalization for near if amblyopia is

present

*

*Bimedial anchored hang back recession

with or without faden sutures .

*Surgical correction of other EOMs

anomalies

Page 12: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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*

*NBS

*Variable angle

*Stable large angle that disappears

under G.A.

Page 13: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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*

*Partially accommodative esotropia

*Angle not corrected under G.A

*

*Premacular esotropia

*Postmacular esotropia

Page 14: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

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*

*Better for postmacular esotropia

*

*Residual esotropia 5-10%

*Consecutive exotropia (late) 30%

Page 15: Mahmoud Aly Rageh , MD.€¦ · Congenital Esotropia * Essential infantile Esotropia *Idiopathic infantile Esotropia *Early onset Esotropia *Early Acquired Esotropia *Ciancia’s

1/29/2018

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**Immediate

*

*