injuria celular - acumulaciones
DESCRIPTION
Injuria celular acumulaciones - Dra. JaraTRANSCRIPT
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INJURIA CELULAR INJURIA CELULAR ENFERMEDADES POR ACUMULACION ENFERMEDADES POR ACUMULACION
Dr.HERBERT ANGELES VILLANUEVA
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LESION CELULAR LESION CELULAR
Noxa ?
INJURIA
ACUMULACIONES INTRACELULARES
1. SUSTANCIA ENDOGENA NORMAL O EN EXCESO
2. SUSTANCIA ENDOGENA NORMAL O ANORMAL
3. SUSTANCIA EXOGENA ANORMAL
-ALTERACION DEL EQUILIBRIO IONICO.-ALTERACIONES METABOLICAS
-DISRUPCION DE PROTEINAS
MINERALES-PRODUCTOS DE AGENTES INFECCIOSOS
PIGMENTOSINCLUSIONES VIRALES
-Por defectos genéticos o Adquiridos en el:
METABOLISMOEMPAQUETAMIENTO
TRANSPORTE SECRECION
AGUACARBOHIDRATOS
LIPIDOS,PROTEINAS
Alteración en:DEGRADACION TRANSPORTE
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MECANISMOS GENERALESMECANISMOS GENERALESDE LA ACUMULACION CELULARDE LA ACUMULACION CELULAR
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ACUMULACION DE LIPIDOSACUMULACION DE LIPIDOS
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ATEROESCLEROSIS
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ATEROESCLEROSISATEROESCLEROSIS
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Acumulaciones intracelulares: Acumulaciones intracelulares: AteroesclerosisAteroesclerosis
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ESTEATOSIS GRASAESTEATOSIS GRASA
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ACUMULACION DE PRODUCTOS DE ALMACENAJEACUMULACION DE PRODUCTOS DE ALMACENAJE
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ACUMULACION DE ACUMULACION DE CARBOHIDRATOSCARBOHIDRATOS
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DIABETES MELLITUS
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ENFERMEDAD DE MAC ARDLE-ENFERMEDAD DE MACK ARDLE
Deficit de fosforilasa muscular
Hepatomegalia
Hipoglicemia
Debilidad muscularCalambres↑ lactato tras ejercicio
ENFERMEDADES POR ALMACENAMIENTO DE GLUCOGENO
ENFERMEDAD DE VON GIERKE
deficit de Glucosa 6 fosfatasa
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ACUMULACION DE PROTEINASACUMULACION DE PROTEINAS
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HEPATITIS ALCOHOLICA
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HEPATITIS C
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ENFERMEDAD DE ALZHEIMERENFERMEDAD DE ALZHEIMER
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DEFICIENCIA DE ALFA-1-ANTITRIPSINA)DEFICIENCIA DE ALFA-1-ANTITRIPSINA)
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PLASMOCITOMA
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ACUMULACIONES ACUMULACIONES EXTRACELULARESEXTRACELULARES
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AMILOIDOSIS
Colorac. Rojo de congo
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ACUMULACION DE LIPOFUCSINA
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ACUMULACION DE PIGMENTOSACUMULACION DE PIGMENTOS
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ACUMULACION DE HEMOSIDERINA
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ACUMULACION DE HEMOSIDERINA (H)
Reacción de Prusia
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Acumulación de Hemosiderina (R)
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IICTERICIACTERICIA
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COLESTASISCOLESTASIS
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ACUMULACION DE MELANINAACUMULACION DE MELANINA
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Acumulacion de melaninaAcumulacion de melanina
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ACUMULACION DE PIGMENTOS EXOGENOSACUMULACION DE PIGMENTOS EXOGENOS
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AntracosisAntracosis
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CALCIFICACION PATOLOGICACALCIFICACION PATOLOGICA
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CALCIFICACION PATOLOGICA
CALCIFICACION DISTROFICA
CALCIFICACION METASTASICA
CAUSA
PATOGENESIS
CUADRO CLINICO
MORFOLOGIA
EDAD Y DEGENERACION CELULAR
(CALCIO SERICO NORMAL)
HIPERCALCEMIA
FORMACION DE CRISTALES DE CA Y FOSFATO
MATERIAL GRANULAR BASOFILO INTRA Y EXTRACELULAR EN AREASDE NECROSIS Y DEGENERACION
DISFUNCION DEL ORGANO
FORMACION DE CRISTALES DE CA++ y FOSFORO
GENERALMENTE NO DISFUNCION CLINICA
SOLO EN COMPROMISO MASIVO.
DEPOSITOS AMORFOS BASOFILOS NO CRISTALINOS EN ORGANOS SANOS.
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CALCIFICACION PATOLOGICACALCIFICACION PATOLOGICA
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DEGENERACION HIALINADEGENERACION HIALINA
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DEGENERACION HIALINA
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MUCHAS GRACIAS