understanding apraxia in children with down syndrome · understanding apraxia in children with down...
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![Page 1: Understanding Apraxia in Children with Down Syndrome · Understanding Apraxia in Children with Down Syndrome Jennifer Meyers Bekins, MS, CCC-SLP Speech Language Pathologist, II The](https://reader033.vdocuments.us/reader033/viewer/2022042613/5f98cbe3d5e7c066df6ff597/html5/thumbnails/1.jpg)
Understanding Apraxia in Children
with Down Syndrome
Jennifer Meyers Bekins, MS, CCC-SLP
Speech Language Pathologist, II
The Jane and Richard Thomas Center
for Down Syndrome
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Speech Disorders and DS
• Isn‟t it just “Down
syndrome speech?”
• What‟s the difference
between each disorder?
• Why do some children
have very clear
speech?
• Does the type of
speech disorder even
matter?
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Speech Influences in DS
• Smaller than average oral cavity (giving the
impression of a larger tongue)
• Hypotonia of the muscles around the mouth
• Fusion of the lip muscles
• Extra lip musculature
• Neurological differences contributing to
reduced speed and range of movement
• Phonological errors
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Speech All-Stars Video (Removed)
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Research and Speech
• How does research help us treat a child‟s
speech disorder?
• How do we know a certain treatment is best?
• How do I know if I am choosing the right
intervention methods?
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Articulation Disorder: Diagnosis
• Diagnosis: - One or a few sound
errors
- A child may substitute
the “y” in the word
yes with a /w/ changing
the word to “wes”
- Even a few errors may
make it hard for people
to understand your child
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• Largely unknown
• In children with Down syndrome this may be
related to: – Structural differences in the mouth
– Persistent ear infections or fluid-filled ears
– Other health problems that interrupt development
• Is different from dysarthria (muscle
weakness), apraxia (muscle coordination), or
phonological disorder
Articulation Disorder: Cause
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Articulation Disorder: Treatment
• Treatment:
– Show how to produce
the sound correctly
– Teach the child to
recognize correct and
incorrect sound
productions
– Practice sounds
Link:
Articulation
Disorders and
Treatment
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Phonological Disorders: Diagnosis
• This disorder is related to the rules of speech
production
• Children naturally simplify speech as they are
learning to talk – this is called using
phonological processes
• Eventual replacement of this child-like form in
typical development
• Continued use of processes may lead to a
phonological disorder diagnosis
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• A language disorder in speech‟s clothing
Phonological Disorders in DS
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Phonological Disorders in DS
• Not related muscle weakness or poor
coordination
• Difficulty organizing sounds and
understanding the rules that govern their
production
• Ultimately a language problem
• Techniques that focus on strength or
coordination often prove ineffective when
trying to improve speech accuracy
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Phonological Disorders: Treatment
• Therapy targets
each process or
class of sounds
• Starts with group of
sounds that mature
or are established
first
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Apraxia in DS: Diagnosis
• Motor speech disorder
• It is not due to muscle weakness
• Brain has difficulty planning the movements
of the muscles that create speech
• Other signs of apraxia include:
– Limited consonant and vowels
– An appearance of „groping‟ movements
– Inconsistent sound errors that are not the result of
immaturity or other speech disorder
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Apraxia in DS
“The possibility of
dyspraxia as a
diagnosis in DS has
been little investigated.”
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“…Impaired motor function is
not due to cognitive delay, but is
a syndrome-specific
impairment, which may lead to
speech disorder. …the speech
disorder in DS is not related to
cognitive or language level.”
Cleland, et all, 2009
Link: Apraxia
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Incidence
• 1 in 1000 or 3-5% of
preschoolers with
speech disorders
• DS – 15% or 243 in
1620 (Kumin, 2006)
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“Speech disorder in DS
not wholly accounted
for by phonological
delays/disorders or
hypotonicty…the
children do present with
difficulties in motor
planning and
programming.”
Cleland et al, 2010
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Apraxia and DS
• Difficulty achieving and
maintaining articulatory
configurations
• Limited consonant and
vowel repertoire
• Presence of vowel
distortions
• Use of simple syllable
shapes
• Groping
• Inconsistent Errors
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Apraxia and DS
• Difficulty with motor and
linguistic processing
• Impairments of
language and motor
systems
• Motor deficits influence
the development of
phonology and other
language processes
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Treatment Planning
• Determine the
relative contribution
of language to motor
deficits
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Precursors to motor learning
• Development of
trust
• Motivation
• Attention –
maintenance and
effort
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Challenges to motor learning in DS
• Processing speed
• Working memory
• Attention
• Receptive language
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Interest = Attention
• Use motivating toys (dolls, puppets, action
figures)
• Changing positions
• Change inflection (once child has accurate
movement and rate)
– Sing - Vary pitch
– Vary intonation - Vary emotion
– Exaggerate
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Treatment Approach in DS
• Use an techniques
that capitalize on
visual learning
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Treatment Approach in DS
• Start with limited number of stimuli
• Model
• Child imitation
• Slow rate of speech (increases sensory motor
feedback)
• Use tactile cues as needed
• Type of practice (block vs. random)
• Knowing when to choose targets based on
sounds or sound classes
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Choosing your stimuli
• Length
• Sound complexity
• Syllable shape (e.g.
CV, VC, CVC,
CVCV, etc.)
• Real or non-sense?
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Apraxia in DS
• Videos
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How do I get them to work???
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Developing Treatment
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Talking is fun!
• Practical ideas for carry-over of speech
therapy at home (AKA distributed practice)
– Car time
– Daily routines
– Tokens
– Game time
– Containers
– Phone
– Echo Microphone
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Toys for treatment
• Bubbles
• Balloons
• Bowling Set
• Launchers (hot wheels,
motorcycles, wind-up
toys)
• Ball and Hammer toys
• Blocks
• Elefun
• Play Dough
• Potato Head
• Puzzles
• Rice/Beans/Pasta
Container
• Phlat Ball
• Plastic Food
• Play Farm with animals
• Doll House
• Dolls
• Trains
• Candy Land Castle
• Lucky Ducks
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Sign Language
• Do you know Rachel,
Alex, & Leah?
• Dual modality (sign and
speech)↑recognition of
vocab words
Raining Bird, 2000
• Sign is an unaided
system and involves
direct communication
with turn taking and eye
contact
Clibbens, 2001
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How old is too old for therapy?
• Considerations
– Hearing status
– Motivation
– Stimulability
– Motivation
– Working on
communication
strategies
– Motivation
– Family support
– Frequency and
duration of therapy
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Oral Motor and DS
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Oral Motor and DS
• What can it hurt?
• Aren‟t I waking up
muscles needed to
talk?
• What if I use oral motor
along with more
traditional therapies?
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Before and After
• Images removed
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Oral Motor Update
• Negative affect reported when using a
combination approach including oral motor
treatment and traditional approaches
• Had therapy only focused on speech sound
development, these children probably would
have shown progress much sooner.
(In research with cleft palate)
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Buyer Beware!
“In our quest to help … we are always looking
for the newest and best treatments…
Although many of these treatments are valid
and have potential use, many others
advertised may not live up to their promised
result.”
ASHA Leader, July 5, 2011
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What if my child still doesn’t talk?
• Augmentative Communication (AC)
• Will AAC prevent speech from developing?
• Benefits of AC or other forms of assistive
technology (AT)
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Pauses in Progress
• How do I address
plateaus in my
child‟s speech?
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Next Steps
“Clearly more research is needed to clarify the
exact nature and origin of the speech
disorder in DS in order to design appropriate
interventions.”
Cleland, et al 2009
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Contact:
Jennifer Meyers Bekins, MS, CCC-SLP
Speech Language Pathologist, II
The Thomas Center for Down Syndrome
Division of Developmental and Behavioral Pediatrics
Cincinnati Children‟s Hospital Medical Center
3333 Burnet Ave. MLC 4002
Cincinnati, OH 45236
513.636.0520
www.letstalkds.org