SYSTEMIC SCEROSIS(scleroderma)

Generalised disorder of connective tissue affecting•Skin

•Internal organs•Vasculature

CREST syndrome•Calcinosis•Raynaud’s•Esophageal involvement•Sclerodactyly•Telangiectasia

CASE REPORT

A 30 yrs male presented with complaints of• giddiness • Palpitations• Heart burn and indigestion• Decreased vision (Rt eye) with floaters

PAST HISORY15 Yrs back diagnosed as systemic sclerosis with h/o• shiny hard skin (hand)• Blue fingers on winter mornings

2000Bilateral renal calculi

2003Jaw swellingSurgery for calcinosis (thrice)

2005Ankle and shoulderjt pains Asymmetrical,Morning stiffness +RF +kept on steroids

Treated for hypertension

Epistaxis and bleeding gums

EXAMINATION

• Bilateral parotid swelling

Thin lips

TELANGIECTASIA

Hands showing • tight shinyskin,• sclerodactyly• thickening of extensor

tendon sheath

CALCINOSIS

MUSCULOSKELETAL SYSTEM

Stiffness at hip,knee,lower spine

Ophthalmic examination

Visual acuity Right eye Left eye

Without correction

3 mt(cf) 6/60

With correction - 6/6

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