swedish pediatrics pediatric urology team devon snow-lisy...

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Swedish Pediatrics Pediatric urology team Beth Andersen, MD Devon Snow-Lisy MD

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Page 1: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Swedish Pediatrics Pediatric urology team Beth Andersen, MD Devon Snow-Lisy MD

Page 2: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Penis

Page 3: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Physiologic phimosis

• At birth prepuce can be retracted completely in 4% of newborns

• 54% the external meatus can only just be seen • 42% the tip of the glans cannot be seen

– (Gairdner 1949)

Page 4: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Likely there are regional differences in phimosis

• Zheijiang China: high prevalence of physiologic phimosis in kindergarten children, up to 44% at age 6

• Swaziland (preputial adhesions-39% + phimosis-78% + hypospadias-3%:

Page 5: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Inner preputial adhesions in the uncircumcised penis

Page 6: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Abnormal raphe

Page 7: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Abnormal raphe

Page 8: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Penile torsion

• Common 12% of men • Most commonly

counterclockwise • Can be associated

with chordee and identified before circumcision by deviated penile raphe

• More likely to be bothered with increasing severity >45 degrees

Page 9: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Penile Chordee

Page 10: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Penile chordee • Seen in 4-10% of males • Results from disproportionate development of the tunica

albuginea of the corporal bodies. • Untreated patients may have worse penile perception

scores, mentally unhealthy days and increased difficulty with intercourse (> 20 degrees curvature)

• Plication is used almost exclusively with satisfactory curve correction rates in 67-97%.

Page 11: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Inconspicuous penis variants

Page 12: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Penile webbing

Page 13: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Buried penis

Page 14: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Buried penis

After penoplasty

Page 15: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Normal skin fixation in a obese infant

Page 16: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Inconspicuous penis

• When does it “need” to be fixed • UTIs, urine trapping (megaprepuce variant),

recurrent balanitis, continuing phimosis

Page 17: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Open/cleft foreskin

Page 18: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Megameatus variant of hypospadias OK for newborn circumcision if intact prepuce • 93 had an aborted newborn circumcision

– 28 underwent hypospadias repair – 47 underwent circumcision completion under general

anesthesia – 18 either deferred surgery or underwent in-

office circumcision. • 10 had completed circumcision with hypospadias with

intact prepuce – No complications

• 151 control group patients – 5.3% complication rate

• Performing circumcision in newborns with hypospadias and an intact prepuce did not affect repair or the risk of complications.

Page 19: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Proximal shaft hypospadias

Page 20: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Micropenis

(2.5 SD smaller than mean) ie in newborn < 1.9 cm (0.75 inches) Normal stretched penile length length of newborn penis 2.8-4.2 cm

Page 21: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Epispadias

Page 22: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Epispadias

Page 23: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Chronic Complications after Circumcision

• Incomplete circumcision and skin tags • Skin Bridges • Meatitis and meatal stenosis • Secondary phimosis and concealed (buried)

penis • Fistulas and megalourethras • Inclusion cysts

Page 24: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Buried Penis after Newborn Circumcision

• 88 patients with buried penis AFTER newborn circumcision

Patient age (years)

# of Patients

% with Buried penis (#)

Younger than 1

14 100% (1)

1-3 59 32.2% (19) >3 15 6.7% (1)

Page 25: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Trapped Penis after Newborn Circumcision

• Retrospective review • 14 infants with trapped penis • Within 4 weeks of the newborn circumcision • 0.05% Betamethasone cream 3 times daily

for 3 weeks + manual retraction • 78% with improvement/able to retract

behind head of the penis • 21% required formal reconstruction

Page 26: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Incomplete Circumcisions

Insufficient skin and insufficient inner prepuce is removed

Skin did not necrose or was left

Chronic Complications

Page 27: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Adhesions

Pathologic

Chronic Complications

0%

10%

20%

30%

40%

50%

60%

70%

80%

Fine adhesions to thecorona

Adhesions coveringless than 50% of glans

Adhesions covering>50% of glans

Total Adhesions

less than 1 year old 1 to 5 years 5 to 9 years over 9 years

Page 28: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Chronic Complications-Skin Bridging

Page 29: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Chronic Complications-Skin Bridging

Page 30: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Chronic Complications-Unusual Skin Bridging

Page 31: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Presumably develops secondary to diaper dermatitis with subsequent scarring

Chronic Complications-Meatal Stenosis

Page 32: Swedish Pediatrics Pediatric urology team Devon Snow-Lisy MD/media/Images/Swedish/CME1...Inconspicuous penis variants . Penile webbing . Buried penis . Buried penis . After penoplasty

Questions?