simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

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RHEUMATIC HEART DISEASE What are the Consequences? Nahar Taufiq Bagian Kardiologi Kedokteran Vaskuler FK UGM KSM Jantung RSUP DR Sardjito Jogjakarta

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Page 1: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

RHEUMATIC HEART

DISEASEWhat are the Consequences?

Nahar TaufiqBagian Kardiologi Kedokteran Vaskuler FK UGM

KSM Jantung RSUP DR SardjitoJogjakarta

Page 2: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Acute Rhematic Fever (RF) and

Rhematic heart disease (RHD)

Consequences of Haemodynamic

When to Intervention?

Consequences of Anticoagulant Therapy

An Overview

Page 3: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Rhematic Fever (RF) and or Rhematic

heart disease (RHD) is a a major health

hazard in most developing countries as well

as sporadically in developed economies

Rheumatic Heart Disease

Page 4: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

RF and RHD are systemic inflamatory

disease with protean manifestation

primarily affecting the connective tissue

and usually preceded by a group A beta

hemolytic streptococcal (GABHS)

infection characterized by acute

exacerbation and recurrencces

Rheumatic Heart Disease

Page 5: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Infection by GABHS

2 – 5 days intubation

URI infectionhigh fever, sore throat, headache, body weakness,

and increase in WBC count

Acute Rheumatic Fever

Acute Rheumatic Heart Disease

3% of them develop RF after

Several weeks

Major : Carditis, Polyarthritis,Chorea,

erythema marginatum, Subcutaneus nodule

Minor : Clinis : arthralgia , fever

Lab : Erythrocyt cedimen rate, C – reactive protein

prolonged PR interval,positive throat culture,etc

2 Major or 1 major 2 minor

Evidence for recent GAS infection

Page 6: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Acute Rheumatic heart disease

Divided into rheumatic endocarditis,

rheumatic myocarditis

and rheumatic pericarditis,

often for rheumatic pancarditis.

Page 7: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Management ARF-ARHD

1. Eradicate the GAS

Benzathine Penicilin G ,

< 27 kg : 600.000 U –IM (once)

> 27 kg : 1,200,000 U – IM (once)

Erythromycin estolate, 20-40mg/kg/2-4 times daily ( 10

days)

Erythromycin Ethylsuccinate 40mg/kg/2-4 times (max 1

g/d) (10 days)

Page 8: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Management ARF-ARHD

2. Suppress the Inflamatory response

Aspirin 90-120 mg/kg/day for 10 weeks and tapered in the

next 2 weeks

> 20 kg: Prednison 60 mg/day three weeks and tapered in

the next nine weeks

< 20 kg : prednison 40 md/day

Page 9: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Secondary Prevention of RF

• Benzathine Penicilin G 1,200,000/ 3-4 weeks – IM

• Penicilin V 25 mg twice daily – oral

• Erythromycin 250 mg twice daily -oral

Page 10: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Acute Rheumatic Fever

Acute Rheumatic Heart Disease

Acute rheumatic endocarditis: small (diameter 1- to 2-mm)

vegetations along the mitral valve margin, insufficient to

cause valvular deformation.

Page 11: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Chronic Rheumatic Heart Disease

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Mitral Regurgitation

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Mitral Regurgitation

Page 17: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Mitral Regurgitation

Page 18: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Mitral Regurgitation

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Mitral Regurgitation

Porcine model, 6M

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Mitral Stenosis

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Mitral Stenosis

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Mitral Stenosis

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Mitral Stenosis

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Mitral Stenosis

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Due to the vibration of the anterior leaflet of the mitral

valve as it is buffetted simultaneously by the blood jets

from the left atrium and the aorta.

Aortic Regurgitation

Aortic Regurg – Austin Flint Murmur

Page 28: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Aortic Regurgitation

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Aortic Regurgitation

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Aortic Regurgitation

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Aortic Regurgitation

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Aortic Stenotic

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Aortic Stenotic

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TERIMA

KASIH

Page 43: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Dr. T Duckett Jones

- Major Manifestation

- Carditis, Arthritis, subcutaneous nodules,

erythema marginatum and chorea

- Minor manifestation

- Fever, arthralgia

- Essensial Criteria

Acute Rheumatic Fever

Acute Rheumatic Heart Disease

Page 44: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Acute rheumatic endocarditis: small (diameter 1- to 2-mm) vegetations along the mitral valve

margin, insufficient to cause valvular deformation.

Page 45: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Small vegetations (verruca) are visible along the line

of closure of the mitral valve leaflet (arrows).

Page 46: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Advanced: vegetations organization, recurrent organization cause chronic heart valve disease (

valvular stenosis and / or valvular insufficiency )

Page 47: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk
Page 48: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Mitral stenosis with diffuse fibrous thickening and distortion of

the valve leaflets, commissural fusion (arrows), and thickening

and shortening of the chordae tendineae.

Page 49: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Rhematic Fever (RF) and or Rhematic

heart disease (RHD) is a systemic

inflamatory disease with protean

manifestation primarily affecting the

connective tissue and usually preceded

by a group A beta hemolytic streptococcal

(GABHS) infection characterized by acute

exacerbation and recurrencces

Rheumatic Heart Disease

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Page 58: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Template Jogja Cardiology Update

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Page 59: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

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Page 60: Simposium iii. 1. rheumatic heart disease. dr. nahar t. spjpk

Jogja Cardiology Update Jogja Cardiology

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