pulmonary hypertension

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BY DR LAILA PULMONARY HYPERTENSION

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Page 1: Pulmonary hypertension

BY

DR LAILA

PULMONARY HYPERTENSION

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• Pulmonary vascular circuit has a very low resistance

• Carries a volume of 70ml of blood.

NORMAL

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Normally Increased blood flow in lung bases

as compared to the apices d/t

gravity

NORMAL PULMONARY VASCULATURE

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Minimal blood flow to apices

• Inadequate LA pressure

• Vessel diameter in upper intercostal spaces is not more than 3mm

• Main pulmonary artery diameter is 16mm in males and 15mm in females.

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An increase in blood pressure in the pulmonary artery, pulmonary vein, or pulmonary capillaries, together known as the lung vasculature, leading to shortness of breath, dizziness, fainting n eventually heart failure

Pulmonary hypertension

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Sustained elevation of mean pulmonary arterial pressure to greater than 25 mmHg at rest

or

more than 30 mmHg during exercise, with normal pulmonary capillary wedge pressure and left ventricular end-diastolic pressure (<15 mm Hg)

PAH

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WHO Classification of pulmonary hypertension

Group 1. Pulmonary artery hypertension (PAH)

   Idiopathic Familial

Group 2. Pulmonary hypertension with left heart diseaseGroup 3. Pulmonary hypertension associated with lung disease and/or hypoxaemiaGroup 4. Pulmonary hypertension due to chronic thrombotic and/or embolic diseaseGroup 5. Miscellaneous (sarcoidosis, histiocytosis X, lymphangiomyomatosis, compression of pulmonary vessels)

)

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CXR• Hilar pulmonary arterial dilation.

• Loss of peripheral blood vessel markings

OR

• Peripheral pruning

• Enlarged right atrium and right ventricle in advanced diseases

PAH

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PULMONARY VENOUS HYPERTENSION

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PULMONARY INTERSTITIAL EDEMA

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KERLEY B LINES

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PERIBRONCHIAL CUFFING

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FISSURE EFFUSION

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CEPHALIZATION

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CEPHALIZATION

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PULMONARY ALVEOLAR EDEMA

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PULMONARY ALVEOLAR EDEMA

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PULMONARY ALVEOLAR EDEMA

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PULMONARY HAEMOSIDEROSIS

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Longstanding pulmonary venous HTN leads to pulmonary hemosiderosis (punctate calcific) ossific nodules (< 1cm)

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THANK YOU