osteochondritis dessicans ,caisson disease, caffey’s disease

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OSTEOCHONDRITIS ,Caisson disease, OSTEOCHONDRITIS ,Caisson disease, Caffey’s disease Caffey’s disease

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radiology Osteochondritis dessicans caisson disease caffey’s disease

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Page 1: Osteochondritis dessicans ,caisson disease, caffey’s disease

OSTEOCHONDRITIS ,Caisson disease,OSTEOCHONDRITIS ,Caisson disease,Caffey’s diseaseCaffey’s disease

Page 2: Osteochondritis dessicans ,caisson disease, caffey’s disease

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OSTEOCHONDRITIS DESSICANSOSTEOCHONDRITIS DESSICANSMisnomer.

Refers to post-traumatic osteochondral/chondral fractures.

Occuring at articular surface.

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After injury---detached portion

* remain in situ.

*Mildly displaced.

* Become loose body.

(most common cause of loose body in young adults is OCD)

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Fragmented part—avascular

Bed of defect ---vital

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SITES INVOLEDSITES INVOLED CONVEX ARTICULAR SUFACES:

Medial femoral condyles. Capitellum of humerus. Trochlear surface of talus.

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RARE SITES OF INVOLVMENT:

Shoulder—humeral head ,glenoid. Scaphoid. Navicular.

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INCIDENCEINCIDENCE

M:F =2:1.

One third cases are bilateral.

Adolescence.

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RADIOGRAPHIC FEATURES.RADIOGRAPHIC FEATURES.PLAIN RADIOGRAPHS

May be normal.

When visible =radiolucent ring surrounding bony fragment.

=in profile-loose body opposite to pit in bone.Loss of sharp cortical line of articular surface.

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CT FINDINGS Usually axial cuts.

For cortical defects & loose bodies. Island of bone demarcated by rare field zone.

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MRI FINDINGS vitality of underlying bone integrity of overlying cartilage.

NUCLEAR MEDICINE Non specific mild to moderate increased uptake of isotope in involved bone.

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MRI CLASSIFICATION OF OCDMRI CLASSIFICATION OF OCD STABLE * articular cartilage is breached.

*marrow edema.

UNSTABLE *pocket of fluid around undetached ,undisplaced

fragment.

*displaced osteochondral fragment.

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X-ray knee frontal view---radiolucent line on lateral aspect of medial condyle extending up to articular surface. Joint space normal.

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Lateral radiograph of the knee reveals a calcified loose body (white arrowhead) in the infrapatellar fat pad and lucency in the articular surface of the patella (black arrowhead).

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Ankle frontal view---radiolucent line on dome of talus ,medial aspect. resulting in detachment of fragment. No displacement.

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Axial CT of the knee demonstrates a completely detached osteochondral fracture (arrowhead) in the lateral aspect of the medial femoral condyle.

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Coronal CT of the ankle demonstrates a nondisplaced osteochondral fragment

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CT ankle axial cuts.OCD of talar dome.

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T1W & STIR---coronal & sagittal.unstable.

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Stable –adjacent edema

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Stable OCD –coronal & sagittal T2W shows lesion of medial condyle and marrow edema .

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Coronal T2W unstable OCD with fluid at base of lesion

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CAISSON DISEASECAISSON DISEASE DYSBARIC OSTEONECROSIS.

exposure to hyperbaric atmosphere.

Undersea diving ,space craft.

Result in decompression sickness.

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MECHANISMMECHANISMNitrogen bubbles liberated from bone marrow –

bone infarct by small blood vessel occlusion

Resultant osteonecrosis..

Shoulder most commonly involved.

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PresentationPresentation Joint pain

Motion aggravates pain.

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RADIOGRAPHIC FINDINGSRADIOGRAPHIC FINDINGS Juxta articular defects transradiant subcortical band. collapse of articular cortex. sequestration of articular cortex. secondary osteoarthritis.

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Neck and shaft lesions dense areas. irregular calcified areas.

COMPLICATION

1. Malignant fibrous histiocytoma.

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CAFFEY’S DISEASECAFFEY’S DISEASE INFANTILE CORTICAL HYPEROSTOSIS.

Unknown etiology

In twins ,siblings & cousins.

Remission & relapses with patchy distribution of lesion.

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SITESSITES Mandible.

Ribs.

Clavicle.

Scapulae.

No spine involvement.

Diapysis involvement.

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PRESENTATIONPRESENTATIONChild upto 1 year.

High grade fever & hyperirritability.

Painful deep soft tissue swelling. occur before bone lesion appear.

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RADIOGRAPHIC FEATURESRADIOGRAPHIC FEATURESMarked periosteal proliferation.

Cortical thickening.

Soft tissue swelling.

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OUTCOMEOUTCOMEBone returns to normal by 12 weeks.

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Osteoblastic periosteal lesion involving shaft of ulna ,also lateral aspect of radius.

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Deformity, periosteal reaction. Soft tissue swelling.

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