=Abstract=

Ganglioneuroblastoma with WDHA Syndrome

Dae-Yeon Kim, M.D., Ki-Hong Kim, M.D., Sang-Beom Kim, M.D.,

Sung-Eun Jung, M.D., Seong-Cheol Lee, M.D.,

Kwi-Won Park, M.D., Woo-Ki Kim, M.D.

Department of Surgery, Seoul National University College of Medicine Seoul, Korea

The WDHA syndrome characterized by watery diarrhea, hypokalemia, and achlorhydria (WDHA syndrome) is rare, and with neurogenic tumors. A 20-month-old girl presenting with symptoms of WDHA syndrome was transferred to our hospital. She had a ganglioneuroblastoma of the adrenal gland. The serum level of VIP was elevated. After complete excision of the tumor, all symptoms related to the WDHA syndrome were relieved and serum VIP level dropped to normal. The postoperative course was uneventful. The patient was treated with postoperative chemotherapy and radiation therapy. There was no evidence of disease 33 months after operation.

Index Words: WDHA syndrome, Ganglioneuroblastoma, VIP

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Correspondence : Seong-Cheol Lee, M.D., Department oj

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28 Younkun-dollR, Chon/?Ilo-Ku, Seoul 110-744, Korea

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