female genital development - columbia university · hd-12: female genital development 2 hypospadias...
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HD-12: Female Genital Development
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Female Genital Development
• Normal development• Duplication• Agenesis• UG Sinus• Imperforate hymen• CAH
Dr. Richard Schlussel, M.D., Assistant ProfessorDepartment of Urology, Columbia University
HD-12: Female Genital Development
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Hypospadias Hypospadias repair
Hypospadias repair
• Paramesonephric duct– A.K.A. Mullerian Duct– Becomes future
• Fallopian tubes• Uterus• Upper 2/3 vagina
VAGINAL AND UTERINEDUPLICATION
HD-12: Female Genital Development
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Bicornuate Uterus
Didelphys uterus
Unicornuate UterusComplete Vaginal Duplication
• Symptom– Blood persists despite
tampon duringmenses
• Symptom– Upper vagina fills
with blood duringmenses
HD-12: Female Genital Development
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Mayer-Rokitansky-Küster-Hauser Syndrome
1 in 5,000births
VAGINALAGENSIS
Normal Hymenal Ring
Imperforate hymen
Mucous due to maternalhormones
HD-12: Female Genital Development
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Intra-op drainage of imperf hymenUROGENITAL SINUS
UROGENITAL SINUS
X X
CONGENITAL ADRENAL HYPERPLASIA (CAH)
CAH 46 XX
HD-12: Female Genital Development
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• Association withUrinary TractAnomalies– Renal agenesis– Ectopic ureters