exfoliative dermatitis lopez, camille cecilia s
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EXFOLIATIVE DERMATITISLopez, Camille Cecilia S.
a.k.a. dermatitis exfoliativa, pityriasis rubra (Hebra) & erythroderma (Wilson-Brocq)
- extensive erythema- dull scarlet body surface- small laminated scales- S/s: pruritus, diffuse erythema, epidermal sloughing
malaise, and chills
Andrew’s Diseases of the Skin 9th ed?Medscape
Etiology• Psoriasis• Atopic dermatitis• Chronic actinic
dermatitis• seborrheic dermatitis• Pityriasis• Rubra pilaris• Allergic Contact
dermatitis• Internal Malignancy• Erythrodermic
mycosis fungoides• Sezary synndrome• Medications
PATHOPHYSIOLOGY
Andrew’s Diseases of the Skin 9th ed?Medscape
Increased skin blood perfusion
Temperature dysregulation ( heat loss & hypothermia)
Basal metabolic rate rises
edema, hypoalbuminemia, loss of muscle mass
marked loss of exfoliated scales
In a study of 91 of 102 patients with exfoliative dermatitis by Sigurdsson et al,1 a mortality rate of 43% was observed.
No racial predilection is reported for exfoliative dermatitis.
Male-to-female ratio is 2-4:1 Usually occurs in persons older than 40
years,
TREATMENT
mid- strength corticosteroid after soaking Acitretin, cyclosporin, methotrexate Immunosuppressive agents ( Azathioprine &
Methotrexate)
Andrew’s Diseases of the Skin 9th ed?Medscape