Download - CYANOTIC CONGENITAL HEART DISEASE
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CYANOTIC CHD
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CYANOSISDEFINITION OF CENTRAL CYANOSIS
IT IS BLUE DISCOLOURATION OF THE SKIN & MUCOUS MEMBRANES.IT IS DETECTABLE, WHEN THE DEOXYGENATED HEAMOGLOBIN IS MORE THAN 5 G/100 ML. (capillary) [ OXYGEN SATURATION OF ARTERIAL BLOOD <85% ] 1
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CYANOSIS CLASSIFICATION OF CYANOSIS IN NEWBORN
CENTRAL ( BEST AT TONGUE) : CARDIAC. PULMONARY. NEUROMUSCULAR & C.N.S. PERSISTENT PULMONARY HYPERTENSION. METHAEMOGLOBINAEMIA.. PULMONARY ARTERIOVENOUS FISTULA
PERIPHERAL ( FINGERS & TOES) : PHYSIOLOGICAL ( COLD). REDUCED CARDIAC OUTPUT.
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CONGENITAL HEART DISEASEPRESENTATION
CYANOSIS CYANOSIS WITH DISTRESS
(CYANOSIS WITH HEART FAILURE)
CONGESTIVE HEART FAILURE. SHOCK
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CONGENITAL HEART DISEASEPRESENTATION (CONT..)
CYANOSIS CYANOSIS WITH OBSTRUCTIVE PULMONARY
FLOW .
TRICUSPID ATRESIA, PULMONARY ATRESIA CRITICAL PULMONARY STENOSIS EBSTEIN’S ANOMALY
T.O. F.
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On Clinical Exam ECG X-ray
Variable murmur or none at all
Single S2
Cyanosis tend to be severe
LVH
LAD (0-90)
Generally normal size with elevated apex
Dec PVM
Tricuspid Atresia
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Ebstein's Anomaly
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Ebstein's Anomaly
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Tetralogy of Fallot
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On Clinical Exam ECG X-ray
SEM at 2nd ICS transmitted to back
Single S2
Mild Cyanosis OR no cyanosis
Not in distress
RVH
RAD
Boot shaped heart
Dec PVM
Right arch
Normal
Tetralogy of Fallot
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Tetralogy of Fallot
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PULMONARY ATRESIA
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CONGENITAL HEART DISEASEPRESENTATION (CONT..)
CYANOSIS with increase pulmonary flow (CYANOSIS WITH HEART FAILURE ) :
TRANSPOSITION OF THE GREAT ARTERIES
TOTAL ANOMALOUS PULMONARY VENOUS DRAINAGE.
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Transposition of great arteries
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On Clinical Exam ECG X-ray
Usually no murmur
Single S2
Cyanosis visibly mild may be missed
Comfortable until PDA closes
RVH
May be normal
Generalized cardiomegaly
Narrow mediastinum
Increased PVM
May be normal
Transposition of great arteries
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Transposition of great arteries
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Transposition of great arteries
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CONGENITAL HEART DISEASEPRESENTATION (CONT..)
HEART FAILURE (TACHYPNEA, TACHYCARDIA,SWEATING, PALLOR, POOR FEEDING AND MILD CYANOSIS)
LARGE V.S.D., P.D.A., A.V.S.D. ANOMALOUS L.C.A.
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Atrioventricular Septal Defect
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CONGENITAL HEART DISEASEPRESENTATION (CONT..)
SHOCK COARCTATION OF THE AORTA
CRITICAL AORTIC STENOSIS HYPOPLASTIC LEFT HEART
SYNDROME
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HYPOPLASTIC LEFT HEART SYNDROME
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HYPOPLASTIC LEFT HEART SYNDROME
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HYPOPLASTIC LEFT HEART SYNDROME
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CONGENITAL HEART DISEASEDIAGNOSTIC APPROACH
HISTORY EXAMINATION INVESTIGATION (CHEST X-RAY,
ECG) HYPEROXIC TEST ECHOCARDIOGRAPHY
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CONGENITAL HEART DISEASE CHEST X-RAY
ABNORMAL HEART SIZE ABNORMAL HEART POSITION PULMONARY VASCULAR MARKINGS ABNORMAL HEART SHAPE BOAT-SHAPED HEART:
T.O.F.,TRICUSPID ATRESIA EGG ON SIDE: T.G.A. SNOWMAN: T.A.P.V.D.
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CONGENITAL HEART DISEASEPROSTAGLANDIN INDICATION
CYANOTIC CARDIAC LESION WITH OBSTRUCTION TO PULMONARY BLOOD FLOW
PULMONARY ATRESIA TRICUSPID ATRESIA . CRITICAL PULMONARY VALVE
STENOSIS COMPLEX CYANOTIC C.H.D.
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CONGENITAL HEART DISEASEINDICATION OF PROSTAGLANDIN (CONT..) CYANOTIC LESIONS WITH
CLOSED PULMONARY RECIRCULATION
TRANSPOSITION OF GREAT ARTERIES
TOTAL ANOMALOUS PULMONARY VENOUS DRAINAGE (OBSTRUCTIVE)
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CONGENITAL HEART DISEASEINDICATION OF PROSTAGLANDIN (CONT..) ACYANOTIC LESIONS WITH
OBSTRUCTION OF SYSTEMIC FLOW
COARCTATION OF AORTA INTERRUPTION OF AORTIC ARCH CRITICAL AORTIC STENOSIS HYPOPLASTIC LEFT HEART
SYNDROME