case 2 m-36,erythematous rash on abdomen h/o alport’s syndrome failed renal transplant on...
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Case 2M-36,Erythematous rash on
abdomenH/o Alport’s syndrome
Failed renal transplant on hemodialysis
Clinical presentation Alport’s syndrome diagnosed in 1973 –
progressed to ESRF Cadaveric renal transplant in 1992 CAPD commenced in 2005 Peritonitis and subacute bowel obstruction
necessitated a 2nd Cadaveric renal transplant in 2010 PD port removed in 2011
Presenting Symptoms
Generalised abdominal pain Weight loss 20x15cm erythema in periumbilical area All other investigations negative No response to I/V antibiotics Biopsy performed
REACTIVE ANGIOENDOTHELIOMATOSIS
RAE
Clinically- Erythematous violaceous papules Macules, nodules Cellulitis like areas Seen in abdominal areas, thighs and legs Also seen in other sites
RAE
Represents a hypersensitivity reaction Different stimuli- cryoproteins and
microorganisms Vessel occlusion—hypoxaemia—
endothelial proliferation Reported in association with bacterial
endocarditis and other renal diseases.