blount’s disease
TRANSCRIPT
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BLOUNTS DISEASE
Disusun Oleh :
DODDY TISNA
Pembimbing :Dr. Giri Marsela, Sp.OT
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PENDAHULUAN
Tibia vara dapat terjadi pada setiap kelompok umur
pada anak yang sedang diklasifikasikan sebagai
infantil (1-3 tahun), juvenil (4-10 tahun), dan remaja
(11 tahun atau lebih tua). Prevalensi Bentuk kekanak-kanakan lebih sering
terjadi pada anak perempuan. Bentuk remaja atau
remaja lebih sering terjadi pada anak laki-laki.
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PENDAHULUAN
Kelainan ini lebih sering terjadi pada anak-anak
Amerika Afrika dibandingkan dengan ras lain.
Faktor Risiko untuk penyakit blount, antara lain :
Afrika Amerika etnis, Kegemukan dan Usia diniberjalan. Varus lebih besar pada tibial dari sisi
femoralis adalah faktor risiko untuk penyakit Blount
kekanak-kanakan dan remaja.
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DEFENISI
Tibia vara idiopatik atau penyakit Blount
adalah gangguan yang jarang terjadi yang
ditandai oleh kelainan pertumbuhan sisi media
epifisis tibia proksimal, mengakibatkan
angulasi varus progresif di bawah lutut.
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ETIOLOGI
Penyakit blount terjadi pada anak-anak dan remaja.
Penyebab penyakit ini belum diketahui, tetapi
diperkirakan karena efek dari kelainan pada lempeng
pertumbuhan. Pada komponen bagian dalam tibia tepatnya di bawah
lutut terjadi kegagalan untuk berkembang secara
normal oleh karena adanya angulasi dari tulang.
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ETIOLOGI
Seperti pada bowleg, yang mana cenderung
ditujukan pada perkembangan anak-anak.
Penyakit blount bersifat progresif dan kondisi ini
buruk. Hal ini dapat dikarenakan pembengkokan yang
berat dari kaki dan dapat terjadi pada satu atau
kedua kaki.
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ETIOLOGI
Kondisi seperti ini lebih sering didapati pada
anak-anak keturunan afrika.
Penyakit blount juga dihubungkan dengan suatu
kegemukan, orang-orang pendek dan berjalanbelum saatnya. Penyakit ini tidak bisa
dihubungkan secara jelas dari faktor genetik.
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KLASIFIKASI DAN STAGING
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MANIFESTASI KLINIK
tonjolan metafisis media hebat,
torsi tibia interna,
ketidaksesuaian panjang kaki,
deformitas genu varum progresif lambat, dan
nyeri
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DIAGNOSA
Anamnesa yang lengkap
Pemeriksaan fisik
Pemeriksaan Laboratorium
Pemeriksaan radiologi
Foto Rontgen tibia
CT-Scan
MRI
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DIAGNOSA BANDING
Membungkuk fisiologis kaki
Hypophosphatemic rakhitis
Trauma plat metaphysis atau pertumbuhan
Osteochondroma
Metaphyseal chondrodysplasia
Focal fibrocartilaginous dysplasia
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KOMPLIKASI
Kambuhnya deformitas mengarah ke
ekstremitas keselarasan abnormal dan arthritis
degeneratif.
Limb-panjang bisa mengakibatkan ketimpangan.komplikasi Postosteotomy termasuk komplikasi
neurovaskular dan sindrom kompartemen.
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PROGNOSA
Karena tingkat kekambuhan lebih tinggi pada
pasien dirawat setelah 4 tahun (70-75%)
dibandingkan pada pasien yang diobati sebelum
usia 4 (20-30%), osteotomy dini (sebelum usia4) boleh dilakukan jika bracing tidak berhasil.
Pasien dengan pengobatan terlambat atau
pengobatan tidak lengkap memiliki peningkatan
risiko radang sendi lutut.
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PENATALAKSANAAN
Anjuran diet harian
Anjuran aktifitas fisik harian
Farmakoterapi
Melakukan tindakan umum
Operasi
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DAFTAR RUJUKAN
http://www.patient.co.uk/doctor/Blount%27s-
Disease.htm
http://en.wikipedia.org/wiki/Blount%27s_disease
http://indonesian.orthopaedicclinic.com.sg/?p=900
http://medicalcom.wordpress.com/2011/04/21/tibia-
vara/
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http://www.patient.co.uk/doctor/Blount%27s-Disease.htmhttp://www.patient.co.uk/doctor/Blount%27s-Disease.htmhttp://en.wikipedia.org/wiki/Blount%27s_diseasehttp://indonesian.orthopaedicclinic.com.sg/?p=900http://medicalcom.wordpress.com/2011/04/21/tibia-vara/http://medicalcom.wordpress.com/2011/04/21/tibia-vara/http://medicalcom.wordpress.com/2011/04/21/tibia-vara/http://medicalcom.wordpress.com/2011/04/21/tibia-vara/http://medicalcom.wordpress.com/2011/04/21/tibia-vara/http://indonesian.orthopaedicclinic.com.sg/?p=900http://en.wikipedia.org/wiki/Blount%27s_diseasehttp://www.patient.co.uk/doctor/Blount%27s-Disease.htmhttp://www.patient.co.uk/doctor/Blount%27s-Disease.htmhttp://www.patient.co.uk/doctor/Blount%27s-Disease.htm -
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DAFTAR RUJUKAN
^ Clarke SE, McCarthy JJ, Davidson RS (March 2009). "Treatment of Blount
disease: a comparison between the multiaxial correction system and other external
fixators".J Pediatr Orthop29 (2): 1039. doi:10.1097/BPO.0b013e3181982a62.
PMID19352232. http://meta.wkhealth.com/pt/pt-core/template-
journal/lwwgateway/media/landingpage.htm?issn=0271-
6798&volume=29&issue=2&spage=103. ^synd/1470 at Who Named It?
^ W. P. Blount. Tibia vara: osteochondrosis deformans tibiae. Journal of Bone and
Joint Surgery, Boston, 1937, 19: 1-29.
^ McCarthy JJ, MacIntyre NR, Hooks B, Davidson RS (March 2009). "Double
osteotomy for the treatment of severe Blount disease".J Pediatr Orthop29 (2):
1159. doi:10.1097/BPO.0b013e3181982512. PMID19352234.
http://meta.wkhealth.com/pt/pt-core/template-
journal/lwwgateway/media/landingpage.htm?issn=0271-
6798&volume=29&issue=2&spage=115.
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http://en.wikipedia.org/wiki/Blount's_diseasehttp://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://en.wikipedia.org/wiki/Digital_object_identifierhttp://dx.doi.org/10.1097/BPO.0b013e3181982a62http://en.wikipedia.org/wiki/PubMed_Identifierhttp://www.ncbi.nlm.nih.gov/pubmed/19352232http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://en.wikipedia.org/wiki/Blount's_diseasehttp://www.whonamedit.com/synd.cfm/1470.htmlhttp://en.wikipedia.org/wiki/Who_Named_It?http://en.wikipedia.org/wiki/Blount's_diseasehttp://en.wikipedia.org/wiki/Blount's_diseasehttp://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://en.wikipedia.org/wiki/Digital_object_identifierhttp://dx.doi.org/10.1097/BPO.0b013e3181982512http://en.wikipedia.org/wiki/PubMed_Identifierhttp://www.ncbi.nlm.nih.gov/pubmed/19352234http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://www.ncbi.nlm.nih.gov/pubmed/19352234http://en.wikipedia.org/wiki/PubMed_Identifierhttp://dx.doi.org/10.1097/BPO.0b013e3181982512http://en.wikipedia.org/wiki/Digital_object_identifierhttp://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=115http://en.wikipedia.org/wiki/Blount's_diseasehttp://en.wikipedia.org/wiki/Blount's_diseasehttp://en.wikipedia.org/wiki/Who_Named_It?http://www.whonamedit.com/synd.cfm/1470.htmlhttp://en.wikipedia.org/wiki/Blount's_diseasehttp://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://www.ncbi.nlm.nih.gov/pubmed/19352232http://en.wikipedia.org/wiki/PubMed_Identifierhttp://dx.doi.org/10.1097/BPO.0b013e3181982a62http://en.wikipedia.org/wiki/Digital_object_identifierhttp://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0271-6798&volume=29&issue=2&spage=103http://en.wikipedia.org/wiki/Blount's_disease 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TERIMA KASIH
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