congenital nevi. common malignant neoplasms of infancy and childhoodcommon malignant neoplasms of...

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CONGENITALNEVI

MALIGNANT TUMORS: INCIDENCE & TYPES:

0-4 YEARS 5-9 YEARS 10-14 YEARS

LEUKEMIARETINOBLASTOMANEUROBLASTOMAWILMS TUMORHEPATOBLASTOMASARCOMASTERATOMASMEDULLOBLASTOMA

LEUKEMIARETINOBLASTOMANEUROBLASTOMAHEPATOCA.SARCOMASMEDULLO/ASTROEWING SARCOMALYMPHOMA

HEPATOCA.SARCOMASOSTEOSARCOMATHYROID CAHODGKIN DIS.

Genetic basis (& markers) of some pediatric neoplasias

• Table 10-10, pag. 500.

ALL

THE NEUROBLASTICTUMORS

NEUROBLASTOMA

BILATERAL RETINOBLASTOMA

RETINOBLASTOMA

Wilms’ tumor (nephroblastoma)

Abortive tubules & nephrogenic tissue

Idem

IDEM

Sarcomatoid or sarcomatous stroma

HEPATOBLASTOMA

RABDHOMYOSARCOMA

IDEM

IDEM

IDEM

EWING’S SARCOMA

EWING’S SARCOMA (PNET)

SYMPTOMS?

MAIN SIGN?

TOPOGRAPHY OF THE LESION?

MOST LIKELY NATURE OF IT?

Describe itName of the shown clue…Dx?

Homer-Wright rosettes

WILMS TUMOR: TRIPHASIC PATTERN

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