1. cystic fibrosis
TRANSCRIPT
Cystic FibrosisPediatrics: Respiratory
Cystic fibrosis is serious mucus all over the body, which clogs & damages the lungs, digestive tract, & reproductive organs
Cystic Fibrosis
Chronic hypoxemia (low oxygen) & respiratory infections
1.
Bowel obstruction “Meconium ileus”& Vitamin deficiencies
2.
Weight LOSS & Failure to thrive3.
Diabetes mellitus (HIGH blood sugar)4.
4 NCLEX TIPS
0₂0₂
0₂0₂
B1
C DB12
15kg
>150
Diabetes Mellitus
Children inherit 1 copy of the gene from each parent in order to have the disease.
Sweat chloride test Blood sample
ATI.. child who is suspected of having cystic fibrosis (CF). Which of the following diagnostic tests will confirm the diagnosis?
Sweat chloride test
HESI… child admitted to rule out cystic fibrosis. Which result should be reported to the HCP?
Sweat chloride concentration of 80 mEq/L
Blood sample or sweat test,once the infant is at least 2 weeks old.
2 weeks old
Bowel obstruction “Meconium ileus”
Diabetes Mellitus (HIGH blood sugar) >150
Diabetes Mellitus
Meconium ileus
Since the pancreas is clogged with mucus INsulin cannot get out of the pancreas to put that sugar INto the cell, resulting in diabetes.
HESIQ1: … endocrine disorder commonly found in children with cystic fibrosis?
Diabetes mellitus
Q2: Which is the earliest postnatal manifestation of cystic fibrosis?
Meconium ileus
ATI
Performing chest physiotherapy
A 9 month old infant diagnosed with cystic fibrosis. Which of the following strategies should the nurse explain when instructing the parents?
KAPLAN
The child takes the pancreatic enzymes one hour after eating
Q1: … child diagnosed with cystic fibrosis. The nurse should intervene when:
Increase protein & carbohydrates
Q2: The nurse instructs the parents of a 7-year-old child diagnosed with cystic fibrosis about required dietary modifications.
High caloriesHigh fat, protein, carbohydrates
2 NCLEX TIPS
Complications
Causes
Signs & Symptoms
Nursing Care
Diagnostics
Pathophysiology
Pancreatic Enzymes